Pancytopenia


Hypersplenism

Differential Diagnosis of Splenomegaly and Hypersplenism

Infections
Acute
Viral (viral hepatitis, infectious mononucleosis, CMV infection)
Bacterial (septicemia, salmonellosis, brucellosis, splenic abscess)
Parasite (toxoplasmosis)
Subacute and Chronic
Subacute bacterial endocarditis
Tuberculosis Malaria Kala-azar Fungal disease

Inflammation
Felty syndrome SLE Serum sickness Rheumatic fever Sarcoidosis ALPS

Congestive Splenomegaly
Intrahepatic
Cirrhosis
Extrahepatic
Portal vein obstruction
Splenic vein obstruction
Hepatic vein occlusion (Budd-Chiari syndrome)

Chronic Passive Congestion
Heart failure

Hematologic Disorders
RBC disorders: hemolytic anemias, thalassemia, sickle cell disorders

Neoplasia
Malignant
MPDs Myeloid metaplasia Polycythemia rubra vera Essential thrombocythemia Chronic leukemia Chronic myeloid leukemia Chronic lymphocytic leukemia Hairy cell leukemia Lymphoma Acute leukemia Malignant histiocytosis
Benign
Hamartoma Hemangioma Lymphangioma Fibroma

Storage Diseases
Gaucher disease Niemann-Pick disease

Miscellaneous
Amyloidosis
Cysts

Note: ALPS, Autoimmune lymphoproliferative syndrome; CMV, cytomegalovirus; MPD, myeloproliferative disorder;

 

 


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